# A 6-year-old child with hemophilia A is admitted to the pediatric unit following a fall that resulted in suspected internal bleeding. Which nursing assessment finding would require the most immediate intervention?

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## 문제

A 6-year-old child with hemophilia A is admitted to the pediatric unit following a fall that resulted in suspected internal bleeding. Which nursing assessment finding would require the most immediate intervention?

The nurse is caring for a child with hemophilia A who experienced a traumatic fall.

## 보기

1. Abdominal rigidity with guarding and decreased bowel sounds **✔ 정답**
2. Ecchymosis on the arms and legs from the fall
3. Complaint of mild joint pain in the knees
4. Small hematoma formation at the IV insertion site

**정답: 1**

## 해설

Abdominal rigidity with guarding indicates potential internal abdominal bleeding, which is a life-threatening emergency in hemophilia patients requiring immediate intervention.

This question tests critical thinking about assessment priorities in a pediatric hemophilia patient after trauma. Hemophilia A is a genetic bleeding disorder caused by a deficiency of clotting factor VIII, making patients vulnerable to prolonged bleeding episodes.

Abdominal rigidity and guarding, along with decreased bowel sounds, are classic signs of internal abdominal bleeding or intra-abdominal hemorrhage. In hemophilia patients, even minor trauma can cause severe internal bleeding due to impaired clotting mechanisms. These symptoms suggest intra-abdominal bleeding, which can rapidly progress to hypovolemic shock and death if not treated immediately with clotting factor VIII replacement therapy and possible surgical intervention.

Pathophysiologically, the absence or dysfunction of clotting factor VIII in the intrinsic coagulation pathway prevents proper clot formation. When internal bleeding occurs, the body cannot effectively stop the bleeding, leading to continuous blood loss into body cavities or tissues. Abdominal bleeding is particularly dangerous because the abdominal cavity can accommodate large volumes of blood before symptoms become obvious.

Immediate nursing priorities include assessing vital signs for signs of shock, preparing to administer clotting factor VIII, maintaining IV access, and notifying the physician immediately. The nurse should also prepare for potential blood transfusion and monitor for signs of worsening bleeding. This scenario requires rapid recognition and intervention to prevent life-threatening complications in this vulnerable pediatric population.

## 심화 해설

Clinical Reasoning and Priority Setting in Hemophilia A

When a child with hemophilia A sustains trauma, the nurse must rapidly differentiate between expected superficial bleeding manifestations and signs of life-threatening internal hemorrhage. Hemophilia A is characterized by a deficiency in factor VIII, which disrupts the intrinsic pathway of the coagulation cascade. This impairment prevents stable clot formation, meaning that while small, visible bleeds like ecchymosis are common, the inability to contain bleeding within a closed body cavity can lead to compartment syndrome, organ failure, or hypovolemic shock.

The assessment finding requiring the most immediate intervention is abdominal rigidity with guarding and decreased bowel sounds. This clinical picture is highly suggestive of an intramural hematoma of the gastrointestinal (GI) tract or an intra-abdominal bleed. In individuals with hemophilia, an intramural GI hematoma is a rare but potentially life-threatening manifestation. As the bleeding dissects into the submucosal or subserosal layers of the bowel wall, it can cause intense pain, a rigid, board-like abdomen from peritoneal irritation, and a functional ileus marked by diminished or absent bowel sounds. The rigid abdomen acts as a closed compartment; continued bleeding has no avenue for external decompression, causing a rapid increase in intra-abdominal pressure. This can compress vital vessels, compromise bowel perfusion leading to ischemia or necrosis, and sequester a significant volume of blood, precipitating hypovolemic shock. Prompt identification and timely administration of clotting factor concentrates are of utmost importance for effective management and optimal patient outcomes [1].

The other options, while requiring nursing attention, represent expected or less immediately critical findings in a child with hemophilia following a fall:

- Ecchymosis on the arms and legs is a classic manifestation of a soft-tissue bleed into the skin. Although it can be extensive, it is external to major body cavities and does not pose the same imminent threat of hemodynamic compromise or organ compression.

- A complaint of mild joint pain in the knees signals a hemarthrosis, the most common bleeding episode in hemophilia. While a joint bleed requires prompt factor replacement to prevent chronic arthropathy, it is not immediately life-threatening in the way an expanding intra-abdominal hematoma is.

- A small hematoma formation at the IV insertion site is a localized, superficial bleed. It is easily managed with direct pressure and does not indicate an acute, systemic crisis.

The nurse’s priority is to recognize that abdominal rigidity with guarding represents a closed-space, potentially massive hemorrhage that can rapidly deteriorate into shock. This assessment must trigger an immediate escalation of care, preparation for emergency factor VIII infusion, and notification of the healthcare provider.References (research sources)

- [1]Intramural Hematoma of Gastrointestinal Tract in People with Hemophilia A and B.Research articleTeng WJ, Kung CH, Cheng MM, Tsai JR, Chang CY. (2023) · DOI: 10.3390/jcm12093093

## 임상 시나리오

Hemophilia A: Recognizing Internal HemorrhagePrioritizing life-threatening closed-cavity bleeds over superficial manifestations
In a child with hemophilia A post-trauma, abdominal rigidity with guarding and decreased bowel sounds is the highest priority finding. This presentation strongly suggests an intramural GI hematoma or intra-abdominal bleed, a life-threatening emergency.

A rigid abdomen acts as a closed compartment. Ongoing bleeding increases intra-abdominal pressure, which can rapidly lead to bowel ischemia, necrosis, compartment syndrome, and hypovolemic shock.

CautionDo not delay intervention for visible, superficial bleeding. Ecchymosis, hemarthrosis, and small IV site hematomas are expected and managed with factor replacement and local measures. A rigid abdomen requires immediate notification of the provider and preparation for urgent factor VIII infusion and possible surgical intervention.

## 핵심 개념

- **Hemophilia A** — An X-linked recessive bleeding disorder caused by a deficiency in coagulation factor VIII, leading to impaired clot formation.
- **Intramural Hematoma** — A rare, life-threatening bleed in hemophilia where blood dissects into the bowel wall layers, causing pain, rigidity, and ileus.
- **Guarding** — Involuntary tensing of the abdominal muscles upon palpation, indicating peritoneal irritation from internal bleeding or inflammation.
- **Compartment Syndrome** — A dangerous condition where increased pressure within a closed anatomical space compromises circulation and tissue perfusion, potentially leading to necrosis.
- **Hemarthrosis** — Bleeding into a joint space, a common complication of hemophilia that causes pain, swelling, and limited range of motion.

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