# A 65-year-old male client with amyotrophic lateral sclerosis (ALS) is being assessed by the nurse. Which assessment finding would be most concerning and require immediate nursing intervention? > source: MyMerci (mymerci.kr) > url: https://mymerci.kr/pages/nclex_q.php?qn_id=541217 > language: ko > subject: Adult Health ## 문제 A 65-year-old male client with amyotrophic lateral sclerosis (ALS) is being assessed by the nurse. Which assessment finding would be most concerning and require immediate nursing intervention? ## 보기 1. Muscle fasciculations in the arms and legs 2. Difficulty with fine motor tasks such as buttoning clothes 3. Emotional lability with episodes of inappropriate crying 4. Decreased breath sounds in the lower lung fields with shallow respirations **✔ 정답** **정답: 4** ## 해설 Decreased breath sounds with shallow respirations indicate respiratory muscle weakness, a life-threatening complication in ALS requiring immediate intervention. Other findings like fasciculations, fine motor difficulty, and emotional lability are less urgent. ## 심화 해설 Clinical Reasoning and Priority Setting The most concerning finding is decreased breath sounds in the lower lung fields with shallow respirations. This assessment indicates hypoventilation and impending respiratory failure, which is the leading cause of death in amyotrophic lateral sclerosis (ALS). In ALS, progressive degeneration of both upper and lower motor neurons leads to weakness of the diaphragm and intercostal muscles. When breath sounds diminish in the bases and the respiratory pattern becomes shallow, it signals that the patient can no longer maintain adequate tidal volume or effective gas exchange. This is a life-threatening emergency requiring immediate intervention, such as alerting the provider, preparing for noninvasive ventilation support, and obtaining arterial blood gas analysis. Why the Other Options Are Lower Priority Muscle fasciculations in the arms and legs (Option 1) are a hallmark sign of lower motor neuron involvement in ALS. While distressing to observe, fasciculations are an expected manifestation of the disease process and do not represent an acute threat to airway, breathing, or circulation. They require monitoring and documentation but not emergency intervention. Difficulty with fine motor tasks such as buttoning clothes (Option 2) reflects progressive upper extremity weakness and loss of motor function. This finding is consistent with disease progression and warrants occupational therapy referral and adaptive equipment planning. However, it is a chronic functional decline, not an immediate physiological crisis. Emotional lability with episodes of inappropriate crying (Option 3) describes pseudobulbar affect (PBA), a common symptom in ALS resulting from corticobulbar tract degeneration. While this symptom can significantly impact quality of life and requires pharmacological management, it does not pose an imminent risk to the patient’s survival. Respiratory status always takes precedence in the nursing prioritization framework of airway, breathing, and circulation. Pathophysiology and Clinical Significance of Respiratory Compromise in ALS The respiratory system is critically vulnerable in ALS due to progressive denervation of the respiratory muscles. As the phrenic nerve and intercostal nerves lose their motor neuron input, the diaphragm and intercostal muscles atrophy and weaken. This leads to a restrictive ventilatory defect characterized by reduced vital capacity and impaired cough effectiveness. The finding of decreased breath sounds in the lower lung fields with shallow respirations is a late and ominous sign. It suggests that the tidal volume has fallen to a point where air entry is barely perceptible on auscultation, and the patient is at extreme risk for hypercapnic respiratory failure, atelectasis, and secretion retention leading to pneumonia. The case report by Wang et al. (2026) reinforces the heightened and unpredictable sensitivity of ALS patients to any factor that further compromises neuromuscular transmission or respiratory function [1]. The report specifically highlights the high risk of postoperative respiratory failure and the potential for recurarization even after reversal agents are administered [1]. This underscores the principle that ALS patients have a fragile respiratory reserve. Any additional insult — whether pharmacological, metabolic, or infectious — can precipitate rapid decompensation. Therefore, a nurse's detection of shallow respirations and diminished breath sounds must trigger an immediate escalation of care to prevent respiratory arrest [1].References (research sources) - [1]Recurarization after sugammadex reversal in a patient with amyotrophic lateral sclerosis: Case report.Case reportWang YW, Zhang Y, Hu X, Li X, Han L, Wang DX, Ding T. (2026) · DOI: 10.1097/md.0000000000046928 ## 임상 시나리오 ALS Respiratory Emergency RecognitionImpending Respiratory Failure Assessment In ALS, respiratory muscle weakness is the primary cause of mortality. The most critical finding is hypoventilation, indicated by decreased breath sounds in the bases and shallow respirations. This signals the patient cannot maintain adequate tidal volume or gas exchange. Immediate intervention includes notifying the provider, preparing for noninvasive ventilation (e.g., BiPAP), and obtaining an arterial blood gas analysis. CautionDo not delay intervention for signs of respiratory decline. Fasciculations, fine motor loss, and emotional lability are expected ALS manifestations and do not require emergency intervention unless they directly compromise the airway, breathing, or circulation. ## 핵심 개념 - **Amyotrophic Lateral Sclerosis (ALS)** — A progressive neurodegenerative disease affecting upper and lower motor neurons, leading to muscle weakness, atrophy, and ultimately respiratory failure. - **Hypoventilation** — A state of reduced alveolar ventilation resulting in increased carbon dioxide (PaCO2) levels, often indicated by shallow respirations and diminished breath sounds. - **Fasciculations** — Involuntary, visible muscle twitches caused by spontaneous firing of damaged lower motor neurons, a common hallmark of ALS. - **Pseudobulbar Affect** — A neurological condition characterized by involuntary, sudden, and frequent episodes of laughing or crying, often seen in ALS due to disruption of corticobulbar tracts. - **Noninvasive Ventilation (NIV)** — A method of respiratory support, such as BiPAP, that does not require an artificial airway, often used to manage respiratory insufficiency in ALS. ## 같은 주제 문제 - [A nurse is assessing a 58-year-old client with amyotrophic lateral sclerosis (ALS). 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