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학습 자료 둘러보기 →| Concept | Key Takeaway |
|---|---|
| Hemophilia A Pathophysiology | X-linked recessive disorder causing deficiency of clotting factor VIII. Leads to prolonged bleeding after injury or spontaneously into joints/muscles. |
| Head Trauma in Bleeding Disorders | Treat as a high-risk emergency. Neurological symptoms may be delayed. Priority is prophylactic factor replacement to prevent intracranial hemorrhage (ICH). |
| Nursing Priority (ABCs Adaptation) | In bleeding disorders, "C" for Circulation/Clotting can become a primary survey priority after Airway and Breathing in trauma scenarios. |
| Factor Replacement Therapy | Goal: Raise factor level to hemostatic range (often >50% for major trauma). Administered IV. Nurse must monitor for adverse reactions. |
| Scenario | Child WITHOUT Bleeding Disorder | Child WITH Hemophilia A |
|---|---|---|
| Minor Head Bump (Alert, no injury) | Observe at home. Ice pack. Monitor for signs of concussion (vomiting, drowsiness). | Seek immediate medical evaluation. High suspicion for ICH. Requires factor VIII infusion. |
| First-Line Pain Management | Acetaminophen or Ibuprofen may be used. | Key Point! Acetaminophen only. Avoid NSAIDs (ibuprofen, naproxen) and absolutely avoid aspirin due to bleeding risk. |
| Nursing Focus | Neurological assessment (Glasgow Coma Scale - GCS), symptom monitoring. | Neurological assessment AND immediate preparation for definitive treatment (factor replacement). |
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